- Explains all aspects of pulmonary hypertension diagnosis
- Describes management options and related issues, including in patient subsets
- Will serve as a comprehensive, practically oriented reference
This book is intended as a comprehensive, practically oriented reference on pulmonary hypertension within the context of adult congenital heart disease (ACHD).
After an introductory chapter on pathophysiology, the various types of pulmonary hypertension that may be encountered in ACHD are discussed, highlighting the specifics observed within different patient categories. The diagnostic approach is then addressed in detail, and the last section of the book is devoted to management options, from conservative approaches to interventional treatment and the concept of treat and repair.
Management in specific patient subjects, such as pregnant women, Fontan patients, and Down syndrome patients with Eisenmenger syndrome, is fully discussed, and guidance is also provided on palliative care.
Pulmonary arterial hypertension related to congenital heart disease (PAH-CHD), despite significant similarities in lung pathohysiology, differs significantly from other types of PAH in terms of mechanism of onset, natural history and management. Mistakes and pitfalls in the management of patients with PAH-CHD are often related to a lack of knowledge or expertise in this condition.
Pulmonary Hypertension in Adult Congenital Heart Disease will be a valuable resource and learning tool for all who care for patients with ACHD, both in tertiary practice and general cardiology.
Table of ContentsSection 1: The pathophysiology of PAH in ACHD
- 1 Congenital heart defects and Pathology of PAH in CHD: the Heath Edwards paradigm
Section 2: Types of PAH in ACHD
- 2 Classification
- 3 Eisenmenger syndrome: Pathophysiology and Hematologic effects
- 4 PAH in patients with persistent systemic-pulmonary shunts and PAH in patients with small cardiac defects
- 5 PAH in patients with previous reparative surgery
- 6 Segmental PAH
- 7 Pulmonary vascular disease in patients with Fontan-type circulation
- 8 Postcapillary pulmonary hypertension in ACHD
Section 3: The diagnosis of PAH-CHD
- 9 Physical examination and electrocardiogaphy
- 10 Plain chest radiography and comaputed tomography
- 11 Echocardiography
- 12 Cardiac magnetic resonance
- 13 Cardiopulmonary exercise and 6 minute walk testing
- 14 Cardiac catheterisation
Section 4: The management of PAH in ACHD
- 15 Conservative management and recommendations for PAH-CHD
- 16 PAH therapies
- 17 Interventional treatment and the concept of treat and repair
- 18 Eisenmenger Syndrome in patients with Down syndrome
- 19 Pregnancy and contraception
- 20 Training and recommendations for exercise
- 21 Prognostication in PAH-CHD
- 22 Management of Fontan patients
- 23 End of life and palliative care
- 24 Epilogue: PAH in ACHD: a global perspective and future prospects, including research
